Anesthetic challenges in a child with Lowe’s and Fanconi syndrome

Oculocerebrorenal syndrome of Lowe is a rare X-linked metabolic disorder complicated by Fanconi’s syndrome. Anaesthetic management of Lowe syndrome with Fanconi’s syndrome is challenging to the anaesthesiologists in view of difficult airway due to microcephaly, metabolic abnormalities, and risk of peri-operative seizures. We report a successful anaesthetic management of a case of 2-year-old child scheduled for evaluation under anaesthesia following bilateral lens aspiration surgery.