TY - JOUR
T1 - Cardiac tumor in juvenile onset Behçet's disease
T2 - Case report and review of the literature
AU - Adams, Elizabeth E.
AU - Aluquin, Vincent P.R.
AU - Bingham, C. April
AU - Stone, James R.
AU - Pauliks, Linda B.
PY - 2010/2
Y1 - 2010/2
N2 - Behçe;et's disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet's disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart's right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.
AB - Behçe;et's disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet's disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart's right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.
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U2 - 10.1007/s00246-009-9565-4
DO - 10.1007/s00246-009-9565-4
M3 - Article
C2 - 19859764
AN - SCOPUS:77952305962
SN - 0172-0643
VL - 31
SP - 277
EP - 279
JO - Pediatric cardiology
JF - Pediatric cardiology
IS - 2
ER -