Abstract
IPEX Syndrome (immune deficiency, polyendocrinopathy, enteropathy, X-linked) is a disorder or regulatory T cell (Treg) function which can result in early death due to infection or complications related to autoimmunity. Therapeutic options for these patients can include allogeneic stem cell transplantation (SCT) or the use of immunosuppressive regimens to control the manifestations of autoimmunity. We report a patient with IPEX syndrome who was managed with rapamycin and subsequently developed EBV induced lymphoma.
Original language | English (US) |
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Pages (from-to) | 1056-1057 |
Number of pages | 2 |
Journal | Pediatric Blood and Cancer |
Volume | 50 |
Issue number | 5 |
DOIs | |
State | Published - May 2008 |
All Science Journal Classification (ASJC) codes
- Pediatrics, Perinatology, and Child Health
- Hematology
- Oncology