Epstein barr virus induced lymphoma in a child with IPEX syndrome

Kenneth G. Lucas; David Ungar; Melanie Comito; Brandt Groh

doi:10.1002/pbc.21341

Epstein barr virus induced lymphoma in a child with IPEX syndrome

Kenneth G. Lucas, David Ungar, Melanie Comito, Brandt Groh

Research output: Contribution to journal › Article › peer-review

18 Scopus citations

Abstract

IPEX Syndrome (immune deficiency, polyendocrinopathy, enteropathy, X-linked) is a disorder or regulatory T cell (Treg) function which can result in early death due to infection or complications related to autoimmunity. Therapeutic options for these patients can include allogeneic stem cell transplantation (SCT) or the use of immunosuppressive regimens to control the manifestations of autoimmunity. We report a patient with IPEX syndrome who was managed with rapamycin and subsequently developed EBV induced lymphoma.

Original language	English (US)
Pages (from-to)	1056-1057
Number of pages	2
Journal	Pediatric Blood and Cancer
Volume	50
Issue number	5
DOIs	https://doi.org/10.1002/pbc.21341
State	Published - May 2008

All Science Journal Classification (ASJC) codes

Pediatrics, Perinatology, and Child Health
Hematology
Oncology

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10.1002/pbc.21341

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title = "Epstein barr virus induced lymphoma in a child with IPEX syndrome",

abstract = "IPEX Syndrome (immune deficiency, polyendocrinopathy, enteropathy, X-linked) is a disorder or regulatory T cell (Treg) function which can result in early death due to infection or complications related to autoimmunity. Therapeutic options for these patients can include allogeneic stem cell transplantation (SCT) or the use of immunosuppressive regimens to control the manifestations of autoimmunity. We report a patient with IPEX syndrome who was managed with rapamycin and subsequently developed EBV induced lymphoma.",

author = "Lucas, {Kenneth G.} and David Ungar and Melanie Comito and Brandt Groh",

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AU - Ungar, David

AU - Comito, Melanie

AU - Groh, Brandt

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AB - IPEX Syndrome (immune deficiency, polyendocrinopathy, enteropathy, X-linked) is a disorder or regulatory T cell (Treg) function which can result in early death due to infection or complications related to autoimmunity. Therapeutic options for these patients can include allogeneic stem cell transplantation (SCT) or the use of immunosuppressive regimens to control the manifestations of autoimmunity. We report a patient with IPEX syndrome who was managed with rapamycin and subsequently developed EBV induced lymphoma.

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Epstein barr virus induced lymphoma in a child with IPEX syndrome

Abstract

All Science Journal Classification (ASJC) codes

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