@article{fa1bf75f21dc4ea6bf73f610989e5ffc,
title = "Evaluation of the reliability of the Cutaneous Dermatomyositis Disease Area and Severity Index and the Cutaneous Assessment Tool–Binary Method in juvenile dermatomyositis among paediatric dermatologists, rheumatologists and neurologists",
abstract = "Background: The Cutaneous Dermatomyositis Disease Area and Severity Index (CDASI) and Cutaneous Assessment Tool–Binary Method (CAT-BM) have been shown to be reliable and valid outcome measures to assess cutaneous disease in adult dermatomyositis (DM) and juvenile DM (JDM), respectively. Objectives: This study compared the CDASI and CAT-BM for use by paediatric dermatologists, paediatric rheumatologists and paediatric neurologists in patients with JDM. Methods: Five paediatric dermatologists, five paediatric rheumatologists and five paediatric neurologists each evaluated 14 patients with JDM using the CDASI, CAT-BM, and skin Physician Global Assessment (PGA) scales. Inter-rater reliability, intra-rater reliability, construct validity and completion time were compared. Results: Inter-rater reliability for CDASI activity and damage scores was good to moderate for paediatric dermatologists and rheumatologists, but poor for paediatric neurologists. The inter-rater reliability for CAT-BM activity scores was moderate for paediatric dermatologists and rheumatologists, but poor for paediatric neurologists and poor across all specialties for damage scores. Intra-rater reliability for the CDASI and CAT-BM activity and damage scores was moderate to excellent for paediatric dermatologists, rheumatologists and neurologists. Strong associations were found between skin PGA activity and damage scores and CDASI or CAT-BM activity and damage scores, respectively (P < 0·002). The CDASI had a mean completion time of 5·4 min compared with that for the CAT-BM of 3·1 min. Conclusions: Our data confirm the reliability of the CDASI activity and damage scores and the CAT-BM activity scores when used by paediatric dermatologists and rheumatologists in assessing JDM. Significant variation existed in the paediatric neurologists{\textquoteright} scores.",
author = "J. Tiao and R. Feng and Berger, {E. M.} and Brandsema, {J. F.} and Coughlin, {C. C.} and N. Khan and Kichula, {E. A.} and Lerman, {M. A.} and S. Lvovich and McMahon, {P. J.} and Rider, {L. G.} and Rubin, {A. I.} and Scalzi, {L. V.} and Smith, {D. M.} and Taxter, {A. J.} and Treat, {J. R.} and Williams, {R. P.} and Yum, {S. W.} and J. Okawa and Werth, {V. P.}",
note = "Funding Information: We are indebted to the Department of Veterans Affairs Veterans Health Administration, Office of Research and Development, Biomedical Laboratory Research and Development, and the National Institutes of Health (R21 AR066286). Funding for this study was provided by the Edwin & Fannie Gray Hall Center for Human Appearance at the University of Pennsylvania. This work was supported in part by the intramural research program of the National Institutes of Health, National Institute of Environmental Health Sciences. Funding Information: We thank Jordan Achtman, MD, Julie Burroughs, MA, Jessica Haber, MD, Khor Jia Ker, MD, and Jamie Langenhan, MD, for their administrative support. We also thank the following physicians for their assistance in recruiting patients: Bita Arabshahi, MD, of Inova Children's Hospital, Fairfax, VA, U.S.A.; Melissa Lerman, MD, PhD, of the Children's Hospital of Philadelphia, PA, U.S.A.; Paul Rosen, MD, of Nemours, Wilmington, DE, U.S.A.; and Lisabeth Scalzi, MD, MS, of Penn State Children's Hospital, Hershey, PA, U.S.A. We also wish to acknowledge the assistance of the Cure JM Foundation in recruiting patients, as well as Dr Edward Cowen for critically reading the manuscript. Funding Information: 11Environmental Autoimmunity Group. Clinical Research Branch, National Institute of Environmental Health Sciences, National Institutes of Health, Bethesda, MD, U.S.A. 12Penn State Children{\textquoteright}s Hospital, Hershey, PA, U.S.A. 13Minneapolis Clinic of Neurology, Maple Grove, MN, U.S.A Publisher Copyright: {\textcopyright} 2017 British Association of Dermatologists",
year = "2017",
month = oct,
doi = "10.1111/bjd.15596",
language = "English (US)",
volume = "177",
pages = "1086--1092",
journal = "British Journal of Dermatology",
issn = "0007-0963",
publisher = "Wiley-Blackwell",
number = "4",
}