Long segment Hirschsprung's disease in the Waardenburg-Shah syndrome

E. J. Gnananayagam, R. Solomon, Chandran Alexander, S. Anbarasi, S. Sen, P. D. Moses

Research output: Contribution to journalArticlepeer-review

5 Scopus citations

Abstract

Presentation with signs of bowel obstruction in an infant with Waardenburg syndrome should raise the suspicion of aganglionosis. We report such a case of long segment Hirschsprung's disease associated with Waardenburg syndrome. Long term care of such children is fraught with high morbidity and mortality.

Original languageEnglish (US)
Pages (from-to)501-503
Number of pages3
JournalPediatric Surgery International
Volume19
Issue number6
DOIs
StatePublished - Aug 1 2003

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Surgery

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