Stenting of the right ventricular outflow tract after late thrombosis of a modified Blalock-Taussig shunt in an infant with tetralogy of Fallot and right pulmonary artery agenesis

Right pulmonary artery agenesis combined with tetralogy of Fallot is a rare congenital heart disease. Infants with this anomaly are in a high-risk group and often undergoe staged surgical repair with initial systemic-to-pulmonary shunt placement. While the shunt thrombosis may occur, a repeat open surgery could be associated with high risk of unfavorable outcome. In this case, an endovascular repair should be an appropriate option. We present the case of right ventricular outflow tract stenting in an 8-month girl with tetralogy of Fallot and right pulmonary artery agenesis after late thrombosis of the left-sided modified Blalock-Taussig shunt.